Teaching neuroImages: MRI changes in superficial siderosis.
نویسندگان
چکیده
A 41-year-old woman presented with 2 months of dysarthria. Her history included 6 years of unsteadiness resulting in multiple falls and 10 years of intermittent urinary incontinence. She had a history of significant trauma including having been knocked over by a horse and being involved in 2 car accidents, 1 resulting in loss of consciousness and amnesia. On examination, she had finger-nose dysmetria and an ataxic gait. She had normal strength but upgoing plantar reflexes. There was no sensorineural hearing loss. Brain MRI (figures 1 and 2) showed hemosiderin deposition consistent with a diagnosis of superficial siderosis.1,2
منابع مشابه
Teaching NeuroImages: Superficial siderosis due to a dural cervical arteriovenous fistula.
A 58-year-old man presented to our hospital with cerebellar ataxia, pyramidal signs, dysarthria, bilateral deafness, and cognitive impairment. These symptoms were consistent with superficial siderosis (SS) of the CNS, confirmed by MRI (figure A). Cerebral angiography showed a dural arteriovenous fistula perispinal and pontic with venous drainage in the left foramen C1-C2, fed by meningeal branc...
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Superficial siderosis of the central nervous system is secondary to chronic subarachnoid bleeding. However, the underlying etiology is not always detected. Superficial siderosis can be diagnosed at MRI by the presence of a hypointense rim along the brain surface on gradient echo T2W images. The authors report a case of superficial cerebral siderosis where the underlying etiology remained undiag...
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BACKGROUND AND PURPOSE Superficial siderosis of the central nervous system results from chronic bleeding in the superficial layers of the cortex and spinal cord. In cerebral amyloid angiopathy (CAA), there is amyloid deposition in meningeal and meningo-cortical arteries and capillaries, predisposing them to rupture. CAA is frequently associated with Alzheimer disease (AD). METHODS We report a...
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متن کاملA patient with superficial siderosis, intraspinal cyst, low-pressure headache and low-lying cord.
Superficial siderosis is a rare condition caused by deposition of hemosiderin in the central nervous system. In recent years, it has been used to identify dural defects connecting the intrathecal space with the intraspinal fluid-filled collection seen in patients with superficial siderosis. However rare reports describe the association of low-lying cord in superficial siderosis patients. We pre...
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ورودعنوان ژورنال:
- Neurology
دوره 78 18 شماره
صفحات -
تاریخ انتشار 2012